Atypical Moyamoya Disease Associated with Midaortic Syndrome

Abstract We report a case of 4-year-old boy who presented with moyamoya disease associated midaortic syndrome. He had been treated for severe persistent hypertension until he suffered multiple episodes seizure and cerebral ischemic attack. Cerebral angiography showed bilateral terminal internal carotid artery stenosis. Angiographic survey stenosis abdominal aorta proximal renal arteries. This is very rare